Test Code: PNL021

Bardet-Biedl syndrome (25 Genes)

Nephrology
Bardet‑Biedl syndrome (BBS) is a rare, autosomal recessive ciliopathy characterised by multisystem involvement, most notably affecting vision and kidney function, with possible impact on the heart, liver, and digestive system. Common clinical features include obesity, intellectual disability, hypogonadism, and polydactyly. The estimated incidence is approximately 1 in 100,000. To date, mutations in around 25 genes have been identified, with BBS1 and BBS10 being the most frequent, accounting for ~51% and ~20% of cases, respectively.
Sample Type
3 ml peripheral blood in EDTA (purple/pink top) tube
Turnaround Time
3 weeks days
Courier Requirements
Ship overnight at room temperature to receive next day. Do not refrigerate or freeze. Maintain specimen at room temperature.
Pricing

Genes Analyzed

25 genes
ALMS1 ARL6 BBIP1 BBS1 BBS10 BBS12 BBS2 BBS4 BBS5 BBS7 BBS9 C8orf37 CCDC28B CEP290 IFT27 IFT74 IFT172 LZTFL1 MKKS MKS1 MKS3 SDCCAG8 TRIM32 TTC8 WDPCP

Methodology

Capture-based target enrichment and Next Generation Sequencing

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